This is a ventral wall defect in which the bowel usually herniates
into the base of a normally inserted umbilical cord through a patent umbilical
ring.
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- Umbilical cord hernia has
similar morphological features to omphalocele
and both terms have been used interchangeable in perinatal
literature.
- Some authors have described
it as a small omphalocele (1) while other
workers (2) have used the term "transient omphalocele"
to describe a sliding umbilical cord hernia.
- The umbilical cord hernia
is thought to result later in embryogenesis, after completion of the
normal formation of the primitive umbilical ring by the four body folds at
3 weeks, and normal elongation of the intestine into the umbilical celom at about 5 weeks. During weeks 10-12 when the
intestine normally returns to the peritoneal cavity, this process is
interrupted, leaving the intestines in the umbilical cord celom, covered by amnion and chorion
(3).
- Differentiation of
umbilical hernia from omphalocele.
- Morphology of the
umbilical ring.
- normal
insertion of the cord into the umbilical ring with intact skin covering
the ring in umbilical hernia. Rectus muscles
have a normal midline insertion close to the xiphoid.
- large
defect in the umbilical ring involving the adjacent muscles and skin in omphalocele.
- Contents within the
defect.
- intestines
that protrude into the base of the ring in umbilical hernia.
- intestines,
liver and other abdominal viscera may be contained in the omphalocele.
- Associated Anomalies.
- Rare, except for malrotation and volvulus
(1).
- Table comparing omphalocele, gastroschisis
and physiological hernia.
- Knochel
JQ, Lee TG, Melemdez MG, Henderson SH. Fetal
anomalies involving the thorax and abdomen. Radiol
Clin North Am 1982;20:297-310.
- Bromley B, Benacerraf BR. Transient omphalocele.
J Ultrasound Med 1992;12:688-689.
- Achiron
R, Soriano D, Lipitz S
et.al. Fetal midgut herniation into the umbilical cord: improved
definition of ventral abdominal anomaly with the use of transvaginal ultrasound. Ultrasound Obstet Gynecol 1995;6:256-260.