- Located in the midline
between the lambda and bregma.
- Associated with callosal
agenesis and large interhemispheric cyst.
- Cranium bifidum - smooth
defect with sclerotic rim of cortical bone.
- Hydrocephalus (15-80%) from
either aqueductal stenosis, Chiari malformation or Dandy-Walker cyst.
- Polyhydramnios.